POEMS Syndrome: A Case Report from Punjab
نویسندگان
چکیده
The present case showed M protein spike with varying type of plasma dyscarasias, ascites, gynaecomastia, impotence and mild acanthosis. POEMS syndrome is a rare multisystem disorder involving polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes. It usually manifests in 5–6 decade of life with a mean survival period of 8 years. We report a case of a 56 years old male surviving more than 15 years with POEMS syndrome. The pathophysiology and genetics of POEMS syndrome is not well understood. An underlying plasma cell disorder is believed to be responsible for it.
منابع مشابه
گزارش یک مورد نشانگان پوئمز (POEMS SYNDROME) از ایران و مروری بر مقالاتی که در این زمینه منتشر شده است.
The crow-fukas, Takatsuki or POEMS syndrome (The acronym of Polyneuropathy, Organomegaly, endocrinopathy, M component and skin changes), a rare, multisystem disorder associated with osteosclerotic myeloma, is characterize by the combination of plasma cell discrasia with polyneuropathy, organomegaly, endocrinopathy, monoclonal(M) protein, skin changes, as well as various other sign, such...
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POEMS syndrome is a plasmocytic dyscrasia that consists a constellation of polyneuropathy(p), organomegaly(o), endocrinopathy(e), monoclonal gammapathy(m) and skin disorders(s). Herein, we report a case of POEMS syndrome that was referred to  ...
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